JDSE
Journal of Dental Sciences and Education

The Journal of Dental Sciences and Education deals with General Dentistry, Pediatric Dentistry, Restorative Dentistry, Orthodontics, Oral diagnosis and DentomaxilloFacial Radiology, Endodontics, Prosthetic Dentistry, Periodontology, Oral and Maxillofacial Surgery, Oral Implantology, Dental Education and other dentistry fields and accepts articles on these topics. Journal of Dental Science and Education publishes original research articles, review articles, case reports, editorial commentaries, letters to the editor, educational articles, and conference/meeting announcements.

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Case Report
Oral and dental rehabilitation under general anesthesia in a pediatric patient with Smith–Magenis syndrome: first case from Turkiye
Abstract
Smith–Magenis Syndrome (SMS) is a rare, genetically-based syndrome affecting multiple systems. It is characterized by developmental delay, behavioral disorders, and characteristic facial features. While various descriptions of the craniofacial and oral findings of SMS exist in the literature, studies involving dental treatment requirements are quite limited. This study aims to present the oral and dental rehabilitation performed for the second time under general anesthesia in a 9-year-old pediatric patient diagnosed with Smith–Magenis syndrome during the mixed dentition period, who presented to our clinic with pain complaints, and to discuss the challenges of dental management of this rare syndrome in light of the literature.

Keywords : Smith–Magenis syndrome, chromosome deletion (17p11.2), general anesthesia, oral and dental rehabilitation

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Article available in :
Volume 4, Issue 2, 2026
Page : 70-75
https://doi.org/10.51271/JDSE-0080
Article Information
Received : 13 Şub 2026
Accepted : 06 May 2026
Published : 25 May 2026
Corresponding Author :

Hayriye Zehra Türk: Department of Pediatric Dentistry, Faculty of Dentistry, Dicle University, Diyarbakır, Turkiye

[email protected]
Citation : Türk HZ, Akleyin E, Sülü B. Oral and dental rehabilitation under general anesthesia in a pediatric patient with Smith-Magenis syndrome: first case from Turkiye. J Dent Sci Educ. 2026;4(2):70-75.

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